Abstract: Chordomas are the tumors commonly involving base of skull which are predominantly solid in consistency. A cystic chordoma of cavernous sinus is an extremely rare entity and has never been reported. We report a 26- year-old male presenting with gradually progressive right sided sixth nerve palsy and headache. Computerized tomography (CT) scan and Magnetic resonant imaging (MRI ) scan of brain showed a cystic lesion in right cavernous sinus.Patient was successfully treated using transnasal endoscopic trans-sphenoidal approach . Histopathological examination of lesion revealed chordoma.Our case is the first report of such condition. Chordoma should be considered as a differential diagnosis of cystic lesion in parasellar location. We briefly review the radiology, the pathology and management dilemmas of such lesions .