Turkish Neurosurgery
Perinatal presentation of a congenital intramedullary capillary hemangioma in a neonate born with hydrocephalus and paraplegia |
Mohammad Amin Dabbagh Ohadi1, Maroufi Seyed Farzad 1, Tayebi Meybodi Keyvan1, Safavi Moeinadin 2, Nejat Farideh 1, Habibi Zohreh1 |
1Tehran University of Medical Sciences, Pediatric Neurosurgery, Tehran, 2Children Medical Center, Pediatric Pathology, Tehran, |
DOI: 10.5137/1019-5149.JTN.41154-22.2 |
Introduction; Spinal intramedullary capillary hemangioma is a rare condition. Although most spinal/spinal cord hemangiomas are inborn in origin, perinatal presentation is uncommon.
Case Presentation; We present a neonate with an intramedullary hemangioma, born with communicating hydrocephalus and complete paraplegia. Spinal imagining showed an intradural mass with hemorrhagic foci, a low-lying conus medullaris, and scalloping of dorsal elements. Ventriculoperitoneal shunting was performed in an emergent setting, with cerebrospinal fluid showing a brownish appearance with high viscosity which implied a possible old hemorrhage. Tissue sample was taken from the spinal lesion in an elective setting. Histopathological examination revealed capillary lobules and extralobular large vessels resembling abnormal veins.
Discussion/Conclusion; The mentioned clues suggested that this congenital hemangioma had become symptomatic from the prenatal period. Though it is a are event, it should be kept in mind while evaluating a neonate with communicating hydrocephalus and weakness of extremities with or without cutaneous hemangiomatous stigmata.
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Corresponding author : Habibi Zohreh