Turkish Neurosurgery
Perinatal presentation of a congenital intramedullary capillary hemangioma in a neonate born with hydrocephalus and paraplegia
Mohammad Amin Dabbagh Ohadi1, Maroufi Seyed Farzad 1, Tayebi Meybodi Keyvan1, Safavi Moeinadin 2, Nejat Farideh 1, Habibi Zohreh1
1Tehran University of Medical Sciences, Pediatric Neurosurgery, Tehran,
2Children Medical Center, Pediatric Pathology, Tehran,
DOI: 10.5137/1019-5149.JTN.41154-22.2

Introduction; Spinal intramedullary capillary hemangioma is a rare condition. Although most spinal/spinal cord hemangiomas are inborn in origin, perinatal presentation is uncommon. Case Presentation; We present a neonate with an intramedullary hemangioma, born with communicating hydrocephalus and complete paraplegia. Spinal imagining showed an intradural mass with hemorrhagic foci, a low-lying conus medullaris, and scalloping of dorsal elements. Ventriculoperitoneal shunting was performed in an emergent setting, with cerebrospinal fluid showing a brownish appearance with high viscosity which implied a possible old hemorrhage. Tissue sample was taken from the spinal lesion in an elective setting. Histopathological examination revealed capillary lobules and extralobular large vessels resembling abnormal veins. Discussion/Conclusion; The mentioned clues suggested that this congenital hemangioma had become symptomatic from the prenatal period. Though it is a are event, it should be kept in mind while evaluating a neonate with communicating hydrocephalus and weakness of extremities with or without cutaneous hemangiomatous stigmata.

Corresponding author : Habibi Zohreh