Turkish Neurosurgery 2008 , Vol 18 , Num 1
Atypical Teratoid/Rhabdoid Tumors: Imaging Findings of Two Cases and Review of the Literature
Selda TEZ1, Aslı KÖKTENER2, Gülnur GÜLER3, Pınar ÖZIŞIK4
1,2Fatih University, Radiology Department, Ankara, Turkey
3Hacettepe University, Pathology Department, Ankara, Turkey
429 Mayıs Hospital, Neurosurgery Department, Ankara, Turkey
Atypical teratoid/rhabdoid tumor (AT/RT) is a malignant embryonal central nervous system (CNS) tumor, manifesting in children, and composed of rhabdoid cells, with or without fields resembling a classical primitive neuroectodermal tumor (PNET), epithelial tissue and neoplastic mesenchyme. Around 200 cases of CNS AT/RT have been documented in the literature. Although the clinical and pathological findings have been defined in large series previously, and AT/RT has become increasingly recognized, awareness of typical AT/RT is important in making the correct diagnosis of this uncommon but probably underdiagnosed entity. Neuroradiologists rarely mention AT/RT in their differential diagnosis and this paper presents two additional cases in which clinical and pathological findings are combined with neuroradiological presentation. Keywords : Atypical teratoid /rhabdoid tumor, Computerized tomography, Magnetic rezonance imaging
Corresponding author : Selda Tez, mesuttez@yahoo.com