A 22 year old woman with a solid haemangioblastoma in the posterior fossa, cervicomedullary junction and spinal cord is reported. Preoperative magnetic resonans imaging (MRI) provided precise indications of the anatomical location and radiological features of the tumor that facilitated its partial removal by microsurgery. Laboratory investigations showed associated erythroeytosis of the haemangioblastoma. The patient was treated with conventional radiation therapy after attempts at surgical resection failed. Twenty- one months after the operation and twenty months after radiation therapy, the patient was neurologically normal.