Primary Ewing's sarcoma of the cranium is quite uncommon. Pre or peroperative recognition of this disease is important as it leads planning the surgical strategy which effects the prognosis. We present a case of primary Ewing's sarcoma originating from mastoid bone and invading petrous bone, occipital bone, brain, dura, as well as tentarium, transverse sinus, skin and cervical muscles. Radiological and pathological findings were demonstrated.