E-ISSN: 1019-5157 ISSN: 2651-5024
Case Report

Intracranial Neuroenteric Cyst in the Cerebellopontine Angle with Calcified Cyst Wall: A Rare Case Report

ORCID Xiaozhou Zuo , ORCID YiHang Ma , Jun Yang , Chunfa Qian , ORCID Yong Liu , ORCID Yihao Zhu
Nanjing Brain Hospital, Neurosurgery; Department of Neurosurgery, Nanjing Brain Hospital Affiliated Medical University
DOI: 10.5137/1019-5149.JTN.49701-25.2 Article in Press

Abstract

Background: Neuroenteric cysts (NCs) are rare benign lesions believed to originate from ectopic endodermal tissue. They are lined by gastrointestinal or respiratory epithelium capable of secreting mucin. Although most frequently located within the spinal canal, intracranial NCs are exceedingly rare and typically occur ventral to the brainstem.
Case Presentation: We report a case of a young female patient with an NC located in the cerebellopontine angle—an atypical site—exhibiting uncommon imaging features. Radiological evaluation revealed cystic contents with signal intensities similar to cerebrospinal fluid, a partially calcified cyst wall, and mild contrast enhancement. Extensive calcification resulted in firm adhesion to adjacent neurovascular structures. Surgical resection was performed, preserving a small calcified plaque that was tightly adherent to critical surrounding tissues.
Conclusion: This case underscores the importance of including NCs in the differential diagnosis of intracranial cystic lesions, particularly when cyst wall calcification is present. Calcification can significantly influence surgical planning and increase the risk of adhesion to neurovascular structures, necessitating cautious dissection.

Keywords

Neuroenteric Cyst Calcification Cerebellopontine Angle Neuroimaging